ISSN 1006-298X      CN 32-1425/R

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肾脏病与透析肾移植杂志 ›› 2022, Vol. 31 ›› Issue (4): 395-400.DOI: 10.3969/j.issn.1006298X.2022.04.020

• • 上一篇    

伴狼疮样表现的IgG4相关疾病

  

  • 出版日期:2022-08-29 发布日期:2022-08-26

A case of IgG4 related disease with SLElike manifestations#br#
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  • Online:2022-08-29 Published:2022-08-26

摘要: 64岁男性,以皮疹、多处淋巴结肿大起病,尿液检查提示少量蛋白尿,无明显镜下血尿,血清肌酐升高,溶血性贫血,抗核抗体、抗双链DNA抗体阳性,补体下降,血清IgG4水平升高,肾活检病理提示IgG4相关间质性肾炎。结合临床及病理最终诊断伴狼疮样表现的IgG4相关疾病。


关键词: 溶血性贫血, IgG4相关疾病, 系统性红斑狼疮

Abstract: The patient was a male aged 64 year old with the following symptoms: rash and multiple enlarged lymph nodes. Laboratory examination results showed proteinuria, renal dysfunction, hemolytic anemia, antinuclear antibodies (ANAs) positivity, antidsDNA antibodies (AdsDNA) positivity, hypocomplementemia, and elevated serum IgG4 levels. Renal biopsy showed IgG4positiveplasma cell infiltration in renal interstitium. Based on the clinical and pathological manifestations, the patient was final diagnosed as IgG4 related disease with SLElike manifestations.


Key words: hemolytic anemia, IgG4-related disease, systemic lupus erythematosus