关键词: 免疫性全血细胞减少症, 膜增生性肾小球肾炎, 微管状结构, 肾活检

Abstract: An 11-year-old boy presented with massive proteinuria and hematuria. The patient had a history of immunorelated pancytopenia, acquired hemophilia and cerebral infarction. Renal biopsy revealed membranoproliferative glomerulonephritis with occasional thrombotic micro-angiopathy-like lesions. On electron microscopy,there were a lot of microtubules in mesangial and subendothelial region,ranging in size from 8 to 12 nm. The final diagnosis was membranoproliferative glomerulonephritis, which was related to immune complex and thrombotic micro-angiopathy lesions.

Key words: immunorelated pancytopenia, membranoproliferative glomerulonephritis, microtubular structuresrenal biopsy