Abstract:

ABSTRACT   IgG4-related systemic disease represents a recently recognized group of multi-organ diseases characterized by a high level of serum IgG4 and dense infiltration of IgG4-positive cells into multiple organs. The most commonly involved organ was pancreas. In this article, the relevant literatures about the renal involvements of IgG4-related systemic disease will be reviewed.

Key words: IgG4  , plasma cells  , tubulointerstitial nephritis