Abstract: This article retrospectively analyzed the diagnosis and treatment of a patient with pregnancy⁃related atypical hemolytic uremic syndrome (P⁃aHUS) admitted to Sichuan Provincial People􀆳s Hospital, and reviewed the literature. This patient developed acute renal failure, anuria, thrombocytopenia, and microangiopathic hemolytic anemia in the second trimester of pregnancy. She had CFHR3 gene mutation and was diagnosed as pregnancy⁃related atypical hemolytic⁃uremic syndrome. After treatment with steroids, eculizumab, and dialysis, the kidney function recovered and platelets became normal, which provides new ideas and references for the treatment of pregnancy⁃related hemolytic uremic syndrome.

Key words: font-family:Inter, -apple-system, BlinkMacSystemFont, ", font-size:16px, background-color:#F9FAFB, ">pregnancy?associated atypical hemolytic uremic syndrome, eculizumab, gene mutation